Congenital Naevus Sebaceous of Jadassohn in a Neonate: an Early Presentation of a Rare Lesion

Abstract

Naevus sebaceous of Jadassohn is a congenital hamartoma of the skin which, if associated with multisystemic complications, can manifest as linear naevus sebaceous syndrome or Schimmelpenning-Feuerstein-Mims syndrome. Naevus sebaceous is linked to postzygotic mutations, potentially increasing the risk of secondary tumour development within the lesion. Notably, secondary tumour transformation appears to be predominantly observed in adults, leading to controversy regarding the optimal timing for surgical excision. In this report, we describe a unique case of a neonate with a naevus sebaceous of Jadassohn, shedding light on the early onset of this rare lesion.